Cystic fibrosis is a life-threatening, inherited condition that affects mucus-producing cells, including those in the lungs and digestive system. There is currently no cure for cystic fibrosis. Treatment for cystic fibrosis focuses on management of symptoms and improving quality of life. The main goals of treatment for cystic fibrosis include:
* Prevention of lung infections
* Controlling lung infections
* Loosening and removing mucus from the lungs
* Prevention of intestinal blockage
* Treatment of intestinal blockage
* Providing adequate nutrition
Drug Treatment
A number of medications can be helpful in treating various aspects of cystic fibrosis. They include:
* Antibiotics: to treat and/or prevent lung infections
* Mucus thinners: to help loosen mucus and make it easier to clear the lungs
* Bronchodilators: to keep airways open
* Oral pancreatic enzymes: to help the digestive system absorb nutrients
Physical Therapies
Chest physical therapy includes techniques that help loosen mucus secretions so that they can be coughed up more easily. There are also mechanical devices that can help loosen mucus in the lungs. They include mechanical chest clappers, inflatable vibrating vests and breathing devices. Doctors may also recommend pulmonary rehabilitation, which includes exercise training, nutritional counseling, energy-conserving techniques and breathing strategies. Doctors may also recommend oxygen therapy if necessary to supplement blood oxygen levels.
Surgical Treatment
A number of surgical procedures may be helpful as part of treatment for cystic fibrosis. They include:
* Nasal polyp removal: if nasal polyps interfere with breathing
* Endoscopy and lavage: to suction mucus that is obstructing airways
* Feeding tube: if cystic fibrosis interferes with digestion
* Lung transplant: for those with severe breathing problems or life-threatening lung complications.
* Bowel surgery: to remove blockages that develop as a complication of cystic fibrosis
Lifestyle and Home Remedies
Among the most important lifestyle changes involved in treatment for cystic fibrosis is good nutrition. People with cystic fibrosis need about 50% more calories than people who don’t have CF. Good nutrition also helps lung function. Regular exercise helps loosen mucus secretion, and increased fluid intake can thin mucus and make it easier to cough up.
Alternative Therapies
The most important complementary and alternative treatment for cystic fibrosis is better nutrition including taking certain nutritional supplements that help increase digestive enzymes in the system. In addition, herbs such as gingko biloba, bromelain, green tea and cat’s claw can help reduce inflammation and boost immune system function. Therapeutic massage and acupuncture may help enhance lung function and boost the immune system.
Stem Cell Therapy for Cystic Fibrosis
Cystic fibrosis is an ideal candidate for treatment with stem cell therapy because it involves a single gene and affects one easily accessible organ. Early tests with stem cells as a treatment for cystic fibrosis show promise. Research continues into the most effective ways to use stem cells to treat cystic fibrosis.